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Pyle's disease: an incidental finding in a routine dental patient

Department of Oral Medicine and Radiology, Bapuji Dental College and Hospital, Davangere – 577 004, Karnataka, India

*Correspondence to: Dr Veena S Narayananan, Department of Oral Medicine and Radiology, Bapuji Dental College and Hospital, Davangere – 577 004, Karnataka, India; E-mail: veesn{at}rediffmail.com

Received 23 December 2004; revised 4 March 2005; accepted 1 May 2005

Pyle's disease (PD) or metaphyseal dysplasia is an extremely rare genetic disorder, transmitted as an autosomal recessive trait. The peculiarity of the disease is that the striking radiographic manifestations contrast with the relatively normal clinical features. The oral findings and radiographic features of the disease are not well documented. The present paper describes the radiographic features of Pyle's disease in a 17-year-old girl and draws attention to the findings in the jaw bones.

Keywords: Pyle's disease; metaphyseal dysplasia; multiple retained deciduous teeth; Erlenmeyer flask deformity